This is an uncommon condition of the heart that can result in
syncope and/or lethal ventricular arrhythmias. In some patients
there may be a hereditary basis for the disorder but in others
there may be only traces of a familial tendency.
The abnormality present in LQTS is based upon an abnormality in
the way the heart recovers from electrical activation with each
heartbeat. In the majority of instances, there is no predictable
underlying structural heart disease. The diagnosis of LQTS is
usually based upon the presence of certain ìmajor and minor
criteria. These relate to a history of syncope, a family history
of sudden cardiac death as well as certain abnormalities in the
electrocardiogram.
The treatment for LQTS includes the use of beta-blockers in
addition to the possibility of ICD implantation.
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